Mucinous tubule and spindle cell carcinoma (MTSCC) of the kidney is a rare renal tumor generally considered of low malignant potential. Radiological diagnosis of the MTSCC is frequently difficult as those tumors tend to present as more discrete changes than those typical for classical renal cell cancer. The radiological diagnosis of a MTSCC can be challenging. It is important to establish correct diagnosis preoperatively in order to qualify patients for NSS.